OBJECTIVES: Hailey-Hailey disease (HHD), or benign familial pemphigus, is a rare autosomal dominant genodermatosis characterized by the formation of blisters. Eruptions are usually located in large skin folds, and when blisters become infected the condition can be very painful and disabling.…
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Carbon Dioxide Laser Treatment in Hailey-Hailey Disease: A Series of 8 Patiënten.
Getagd met carbon dioxide, Hailey-Hailey disease, laser
Geplaatst in Around the Globe, Treatment and Medication
Geplaatst in Around the Globe, Treatment and Medication
Antidesmoglein antibodies in a patient with Hailey-Hailey disease
Abstract BACKGROUND: Hailey-Hailey disease (HHD) is a rare hereditary disease in which the genetic defect is characterized by mutation in the ATP2C1 gene coding for a transmembrane calcium pump. It is generally considered a non-immunologic acantholytic dermatosis in which direct…
Getagd met acantholysis, antidesmoglein antibodies, Hailey-Hailey disease, transmembrane calcium pump
Geplaatst in Around the Globe, News and Information
Geplaatst in Around the Globe, News and Information
Acantholytic rosacea of the forehead and scalp in a patient with Hailey-Hailey disease
BACKGROUND: Rosacea is a common dermatosis that can involve the bald area of the scalp. We report the case of a man presenting clinical symptoms of rosacea of the forehead and the scalp, but with a histological picture of familial…
Getagd met Acantholytic rosacea, Hailey-Hailey disease, immunofluorescence, Köbner phenomenon, pemphigus
Geplaatst in Around the Globe, News and Information
Geplaatst in Around the Globe, News and Information
Familial benign chronic pemphigus and doxycycline
Background Hailey-Hailey disease (HHD) or familial benign chronic pemphigus is a rare autosomal dominant inherited skin disorder, characterized by flaccid vesicles and erosions on the intertriginous areas. Current treatments are not particularly effective. We report 6 cases dramatically improving with doxycycline.…
Getagd met Doxycycline, Hailey-Hailey disease
Geplaatst in Around the Globe, News and Information, Treatment and Medication
Geplaatst in Around the Globe, News and Information, Treatment and Medication
